Strategy for Bone Conservation in the Two-Stage Correction of Hypertelorism in Craniofrontonasal Dysplasia

J Craniofac Surg. 2020 Sep;31(6):1841-1843. doi: 10.1097/SCS.0000000000006585.

Abstract

Pre-emptive planning to optimize safety and outcome is a defining principle of pediatric craniofacial surgery, in which "procedures that come before" should enhance and not compromise procedures that are planned to follow.A technical modification of fronto-orbital advancement/remodeling in 2-stage hypertelorism surgery for craniofrontonasal dysplasia is presented, where orbital hypertelorism is accompanied by coronal craniosynostosis. Fronto-orbital advancement/remodeling undertaken by this approach preserves bone in the supero-lateral bandeau and provides optimal quality bone stock for the subsequent orbital box shift osteotomy. In this way the second procedure is protected and enhanced by optimal planning of the primary procedure, with potential benefits to safety, quality, and outcome of the final result.

Publication types

  • Case Reports

MeSH terms

  • Craniofacial Abnormalities / complications
  • Craniofacial Abnormalities / surgery*
  • Craniosynostoses / complications
  • Craniosynostoses / surgery
  • Humans
  • Hypertelorism / etiology
  • Hypertelorism / surgery*
  • Orbit / surgery*
  • Plastic Surgery Procedures / methods
  • Surgical Flaps / surgery

Supplementary concepts

  • Craniofrontonasal dysplasia