A rare complication of myocardial ischaemia following single-stage repair in a case of Berry syndrome

Abstract

Berry syndrome is a rare congenital cardiac lesion consisting of a distal aortopulmonary window, the aortic origin of the right pulmonary artery (PA), intact ventricular septum and an interrupted or hypoplastic aortic arch. Different repair techniques have been described in the literature. We report a case of Berry syndrome, in whom myocardial ischaemia developed following direct implantation of the right PA to the main PA, which was resolved using an interposition tube graft.

Keywords: Berry syndrome; Interposition graft; Myocardial ischaemia; Right pulmonary artery.