Complete Response of a Young Woman With MYD88WT Bing-Neel Syndrome on Ibrutinib Monotherapy Following a Single Cycle of B Hyper-CVAD/IT MTX

Clin Lymphoma Myeloma Leuk. 2020 Nov;20(11):e809-e812. doi: 10.1016/j.clml.2020.06.004. Epub 2020 Jun 13.
No abstract available

Keywords: Bruton kinase inhibitor; Lymphoplasmacytic lymphoma; Next-generation sequencing; Precision medicine; Waldenström macroglobulinemia.

Publication types

  • Case Reports

MeSH terms

  • Adenine / analogs & derivatives*
  • Adenine / pharmacology
  • Adenine / therapeutic use
  • Adolescent
  • Agammaglobulinaemia Tyrosine Kinase / antagonists & inhibitors*
  • Female
  • Humans
  • Myeloid Differentiation Factor 88 / drug effects*
  • Piperidines / pharmacology
  • Piperidines / therapeutic use*
  • Syndrome
  • Waldenstrom Macroglobulinemia / drug therapy*

Substances

  • Myeloid Differentiation Factor 88
  • Piperidines
  • ibrutinib
  • Agammaglobulinaemia Tyrosine Kinase
  • Adenine