Neurovascular Behçet's Disease Presenting with Cavernous Sinus Thrombosis: A Rare Case of Assumed Tolosa-Hunt-Like Syndrome

Arch Rheumatol. 2019 Jun 25;35(1):128-131. doi: 10.5606/ArchRheumatol.2020.7351. eCollection 2020 Mar.

Abstract

Behçet's disease (BD) is a rare, chronic, auto-inflammatory disorder of unknown origin. Mucocutaneous lesions and pan-uveitis constitute the hallmark of BD. Additionally, vessels of all sizes and types are affected. In this article, we report a 53-year-old female patient diagnosed with neurovascular BD with diplopia, ipsilateral headache and ophthalmoplegia associated with cavernous sinus thrombosis, leading to Tolosa-Hunt-like syndrome. To our knowledge, this is the first report of a patient with complicated cavernous sinus thrombosis in BD.

Keywords: Cavernous sinus thrombosis; Tolosa-Hunt-like syndrome; neurovascular Behçet's disease.

Publication types

  • Case Reports