Extracerebral choroid plexus papilloma in the pharynx with airway obstruction in a newborn: a case report

BMC Pediatr. 2020 Jul 7;20(1):336. doi: 10.1186/s12887-020-02234-2.

Abstract

Background: Choroid plexus papillomas (CPPs) are rare, usually benign, neoplasms originating in the central nervous system. In this study, we present the first case of a giant airway-obstructing CPP in the pharynx of a newborn.

Case presentation: A cystic mass located in the pharynx was noted in a fetus at the 29th week of gestation. Elective cesarean section was performed at the 38th week of gestation with successful intubation and ex utero intrapartum treatment. On computed tomography, there was a huge airway-obstructing cystic mass in the choana and pharynx. Elective surgery with total excision was performed, and histological examination confirmed the diagnosis of CPP.

Conclusion: We report the first case of an extracerebral airway-obstructing CPP in the pharynx of a newborn. Radiologic examinations are not enough for the diagnosis of CPPs, and complete excision of the tumor with histological confirmation is indispensable for accurate diagnosis and treatment.

Keywords: Airway obstruction; Case report; Choroid plexus papilloma; Newborn.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Airway Obstruction* / diagnostic imaging
  • Airway Obstruction* / etiology
  • Airway Obstruction* / surgery
  • Cesarean Section
  • Female
  • Humans
  • Infant, Newborn
  • Magnetic Resonance Imaging
  • Papilloma, Choroid Plexus* / diagnosis
  • Papilloma, Choroid Plexus* / diagnostic imaging
  • Pharynx
  • Pregnancy
  • Tomography, X-Ray Computed