Vietnamese Case Series of Hirayama Disease

In Vivo. 2020 Jul-Aug;34(4):2153-2157. doi: 10.21873/invivo.12022.

Abstract

Background/aim: Hirayama disease, a rare neurological disorder, is characterized by progressive, asymmetric muscle atrophy of the forearm and hand in young male patients.

Case report: We noted two cases of Hirayama disease that appeared in the right upper limb and identified the cervical neutral and flexion position magnetic resonance imaging (MRI) characteristics.

Conclusion: In the flexion posture, the cervical MRI allows early diagnosis of Hirayama disease and should be considered in patients with the typical clinical symptoms.

Keywords: Hirayama disease; cervical MRI; flexion position; neutral position.

Publication types

  • Case Reports

MeSH terms

  • Asian People
  • Cervical Vertebrae*
  • Humans
  • Magnetic Resonance Imaging
  • Male
  • Spinal Muscular Atrophies of Childhood* / diagnostic imaging

Supplementary concepts

  • Amyotrophy, monomelic