Congenital superior vena cava (SVC) anomalies are not uncommon. However, an absence of a left SVC and an anomalous right SVC without additional congenital heart defects is very rare. We present a 38-year-old male with an 'anomalous SVC' that was found to be descending anterior to the pleural space and draining into the inferior vena cava (IVC) at the level of the right atrium. This was associated with an anomalous right upper and lower pulmonary vein draining into this anomalous SVC. To our knowledge, this combination of congenital anomalies has not been previously described in the medical literature.
Keywords: absent right superior vena cava; adult congenital heart disease; anomalous svc; azygos vein; congenital heart disease.
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