A Different Breed of Wolf: First Known Case of Wolf-Hirschorn Syndrome with Third-degree Atrioventricular Block Requiring Pacemaker Implantation

Robert Lee Percell Jr; Hyacinth C Percell; Keith A Miller

doi:10.19102/icrm.2020.110601

A Different Breed of Wolf: First Known Case of Wolf-Hirschorn Syndrome with Third-degree Atrioventricular Block Requiring Pacemaker Implantation

J Innov Card Rhythm Manag. 2020 Jun 15;11(6):4147-4150. doi: 10.19102/icrm.2020.110601. eCollection 2020 Jun.

Authors

Robert Lee Percell Jr¹, Hyacinth C Percell¹, Keith A Miller¹

Affiliation

¹ Electrophysiology Section, Bryan Heart Institute, Lincoln, NE, USA.

Abstract

We describe a case of a 44-year-old male with a history of Wolf-Hirschorn syndrome (WHS) with seizures and mental retardation who was evaluated for what was thought to be a seizure. He was found to be severely bradycardic with a heart rate of 24 bpm. The electrocardiogram revealed third-degree atrioventricular block and he subsequently underwent an uncomplicated single-chamber pacemaker implantation procedure. This is a unique report given its status as the first described case of bradycardic rhythm abnormalities in a patient with WHS.

Keywords: Arrhythmia; Wolf–Hirschorn syndrome; heart block.

Publication types

Case Reports