Conservative management of Cantrell syndrome: a case report

J Surg Case Rep. 2020 Jun 1;2020(5):rjaa100. doi: 10.1093/jscr/rjaa100. eCollection 2020 May.

Abstract

Cantrell syndrome (CS) is defined as congenital combination of five anomalies: defects at the lower part of the sternum, anterior diaphragm, midline supraumbilical abdominal wall, diaphragmatic pericardium and ectopia cordis. Antenatal screening should be performed to make an accurate prenatal diagnosis. The prognosis is usually poor with a high mortality early in life. The gold standard management is surgery but its prognosis remains poor. In many low-income settings prenatal examinations and surgery treatment are not possible. In the present case, we report a not surgery managed baby affected by CS, with good clinical conditions after 5 months.

Keywords: Cantrell pentalogy; Cantrell syndrome; Case report; Low-income settings.

Publication types

  • Case Reports