A salvage pathway maintains highly functional respiratory complex I

Nat Commun. 2020 Apr 2;11(1):1643. doi: 10.1038/s41467-020-15467-7.

Abstract

Regulation of the turnover of complex I (CI), the largest mitochondrial respiratory chain complex, remains enigmatic despite huge advancement in understanding its structure and the assembly. Here, we report that the NADH-oxidizing N-module of CI is turned over at a higher rate and largely independently of the rest of the complex by mitochondrial matrix protease ClpXP, which selectively removes and degrades damaged subunits. The observed mechanism seems to be a safeguard against the accumulation of dysfunctional CI arising from the inactivation of the N-module subunits due to attrition caused by its constant activity under physiological conditions. This CI salvage pathway maintains highly functional CI through a favorable mechanism that demands much lower energetic cost than de novo synthesis and reassembly of the entire CI. Our results also identify ClpXP activity as an unforeseen target for therapeutic interventions in the large group of mitochondrial diseases characterized by the CI instability.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Electron Transport Complex I / genetics
  • Electron Transport Complex I / metabolism*
  • Endopeptidase Clp / genetics
  • Endopeptidase Clp / metabolism
  • Mice
  • Mice, Knockout
  • Mitochondria / genetics
  • Mitochondria / metabolism
  • Myoblasts / metabolism
  • Protein Subunits / genetics
  • Protein Subunits / metabolism

Substances

  • Protein Subunits
  • CLPP protein, mouse
  • Endopeptidase Clp
  • Electron Transport Complex I