This report presents a very rare case of fibrous tumour in the pulmonary artery. A 32-year-old male patient presented at the First Hospital of Jilin University with the chief complaint of chest pain accompanied by cough and haemoptysis. Laboratory test results showed a D-dimer level of 60 ng/ml, and protein S activity of 51.0%. Echocardiography and enhanced computed tomography (CT) of the lung revealed a thrombus-like mass in the main pulmonary artery trunk, and the left pulmonary artery and its branches. The patient was initially diagnosed with pulmonary embolism, but after performing arterial endarterectomy, the presence of a tumour in the corresponding areas was confirmed. Histopathology and immunohistochemistry indicated the presence of a malignant solitary fibrous tumour. Chemotherapeutic agents were administered following surgery. The patient was prescribed ongoing oral Apatinib (250 mg, once daily) as a tumour-targeting therapy. The patient refused permission for postoperative CT. The patient was still alive at the 2-year follow-up.
Keywords: Solitary fibrous tumour; endarterectomy; right heart catheterization.