A 15-Year-Old Boy with Dyspnea and Vanishing Bones

Am J Respir Crit Care Med. 2020 Aug 1;202(3):451-452. doi: 10.1164/rccm.201907-1339IM.
No abstract available

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Biopsy
  • Bone Density Conservation Agents / therapeutic use
  • Dyspnea
  • Exudates and Transudates
  • Humans
  • Imaging, Three-Dimensional
  • Male
  • Membrane Glycoproteins / metabolism
  • Osteolysis, Essential / diagnostic imaging*
  • Osteolysis, Essential / drug therapy
  • Osteolysis, Essential / metabolism
  • Osteolysis, Essential / pathology
  • Pleural Effusion / diagnostic imaging*
  • Ribs / diagnostic imaging*
  • Ribs / metabolism
  • Ribs / pathology
  • Sirolimus / therapeutic use
  • Tomography, X-Ray Computed
  • Zoledronic Acid / therapeutic use

Substances

  • Bone Density Conservation Agents
  • Membrane Glycoproteins
  • PDPN protein, human
  • Zoledronic Acid
  • Sirolimus