An infant with intradural extramedullary synovial sarcoma: the youngest case in the literature

Turk J Pediatr. 2019;61(5):765-770. doi: 10.24953/turkjped.2019.05.017.

Abstract

Yalçın K, Tüysüz G, Kazan S, Gürer Eİ, Karaali K, Küpesiz A, Güler E. An infant with intradural extramedullary synovial sarcoma: the youngest case in the literature. Turk J Pediatr 2019; 61: 765-770. Spinal cord involvement of synovial sarcoma is extremely rare. So far only two cases have been reported. Herein we describe the youngest case in the literature. She is 14-month-old and first presented with difficulty in walking ongoing for a week. Imagining showed a spinal cord mass at C5-T3 levels. The patient had gone under Decompressive surgery and histopathologic examination of the specimen revealed the presence of synovial sarcoma. Although the tumor regressed after chemotherapy, she was lost due to viral pneumonia. Synovial sarcoma should be kept in mind while evaluating spinal tumors even in infantile group.

Keywords: pediatric tumor; spinal tumor; synovial sarcoma.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Age Factors
  • Female
  • Humans
  • Infant
  • Laminectomy
  • Sarcoma, Synovial / diagnosis*
  • Sarcoma, Synovial / therapy*
  • Spinal Cord Neoplasms / diagnosis*
  • Spinal Cord Neoplasms / therapy*