High homogeneity of MMR deficiency in ovarian cancer

Gynecol Oncol. 2020 Mar;156(3):669-675. doi: 10.1016/j.ygyno.2019.12.031. Epub 2020 Jan 8.

Abstract

Objective: Mismatch repair (MMR) deficiency and Bethesda panel microsatellite instability (MSI) are increasingly analyzed to identify tumors that might benefit from immune checkpoint inhibitors, but tumor heterogeneity is a potential obstacle for such analyses. In ovarian cancer, data on intratumoral heterogeneity of MMR deficiency/MSI are lacking.

Methods: N = 582 ovarian cancers were screened for MMR deficiency by immunohistochemistry (IHC) on a tissue microarray. 10 cases suspect for MMR deficiency were identified among 478 interpretable cancers and repeated IHC on large sections combined with polymerase chain reaction (PCR)-based MSI analysis validated MMR deficiency/MSI in 9 of these tumors.

Results: MMR deficiency/MSI was predominantly seen in endmetrioid cancers (8 of 35, 23%) and also in 1 of 358 serous carcinomas (0.3%), but was absent in 34 mucinous carcinomas, 23 clear cell carcinomas, 17 malignant mixed Mullerian tumors (carcinosarcomas), and 11 mixed carcinomas. MMR deficiency involed protein loss of PMS2/MLH1 in 6 cases and of MSH2 and/or MSH6 in 3 cases. 7 MMR deficient cancers were MSI-high (all endometrioid), one was MSI-low (endometrioid) and one cancer with unequivocal MMR protein loss exhibited microsatellite stability (serous). MLH1 promotor methylation was observed in 4 of 5 endometrioid cancers with MLH1 protein loss. Immunostaining of all available cancer-containing tissue blocks (n = 114) of tumors with confirmed MMR deficiency/MSI revealed uniform MMR status throughout the entire tumor mass.

Conclusions: Our data show that MSI is present in a substantial proportion of endometrioid ovarian cancers but can also occur in other tumor subtypes. MMR deficiency/MSI typically involves the entire tumor mass, suggesting that MMR inactivation occurs early in tumorigenesis in a subset of ovarian cancers.

Keywords: Intratumoral heterogeneity; Microsatellite instability MSI; Mismatch repair deficiency dMMR; Ovarian cancer; Tissue microarray.

MeSH terms

  • Adult
  • Aged
  • Aged, 80 and over
  • Carcinoma, Endometrioid / genetics
  • DNA Mismatch Repair*
  • DNA Repair Enzymes / deficiency*
  • DNA Repair Enzymes / genetics
  • DNA-Binding Proteins / deficiency
  • DNA-Binding Proteins / genetics
  • Female
  • Humans
  • Immunohistochemistry
  • Microsatellite Instability
  • Middle Aged
  • Mismatch Repair Endonuclease PMS2 / deficiency
  • Mismatch Repair Endonuclease PMS2 / genetics
  • MutL Protein Homolog 1 / deficiency
  • MutL Protein Homolog 1 / genetics
  • MutS Homolog 2 Protein / deficiency
  • MutS Homolog 2 Protein / genetics
  • Ovarian Neoplasms / enzymology*
  • Ovarian Neoplasms / genetics*
  • Tissue Array Analysis
  • Young Adult

Substances

  • DNA-Binding Proteins
  • G-T mismatch-binding protein
  • MLH1 protein, human
  • PMS2 protein, human
  • MSH2 protein, human
  • Mismatch Repair Endonuclease PMS2
  • MutL Protein Homolog 1
  • MutS Homolog 2 Protein
  • DNA Repair Enzymes