Females with Cystic Fibrosis Demonstrate a Differential Response Profile to Ivacaftor Compared with Males

Am J Respir Crit Care Med. 2020 Apr 15;201(8):996-998. doi: 10.1164/rccm.201909-1845LE.
No abstract available

Publication types

  • Letter
  • Observational Study
  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adolescent
  • Adult
  • Age Factors
  • Aminophenols / therapeutic use*
  • Body Mass Index
  • Body Weight*
  • Child
  • Chloride Channel Agonists / therapeutic use*
  • Chlorides / analysis*
  • Cystic Fibrosis / drug therapy*
  • Cystic Fibrosis / physiopathology
  • Disease Progression
  • Female
  • Forced Expiratory Volume
  • Humans
  • Male
  • Quinolones / therapeutic use*
  • Sex Factors
  • Sweat / chemistry*
  • Young Adult

Substances

  • Aminophenols
  • Chloride Channel Agonists
  • Chlorides
  • Quinolones
  • ivacaftor