Suprasellar Cyst Presenting With Bobble-Head Doll Syndrome

Roshan George; Luvo Gaxa; Zarina Lockhat; Stevens Kgomotso Hlahla; Cornelis Hendrikus van der Meyden; Ravendran Kisten; Meshack Bida

doi:10.1016/j.wneu.2019.09.131

Suprasellar Cyst Presenting With Bobble-Head Doll Syndrome

World Neurosurg. 2020 Jan:133:80-83. doi: 10.1016/j.wneu.2019.09.131. Epub 2019 Sep 28.

Authors

Roshan George¹, Luvo Gaxa², Zarina Lockhat², Stevens Kgomotso Hlahla³, Cornelis Hendrikus van der Meyden⁴, Ravendran Kisten⁴, Meshack Bida⁵

Affiliations

¹ Department of Radiology, Faculty of Health Sciences, University of Pretoria, Steve Biko Academic Hospital, Pretoria, South Africa. Electronic address: roshangeorge6@gmail.com.
² Department of Radiology, Faculty of Health Sciences, University of Pretoria, Steve Biko Academic Hospital, Pretoria, South Africa.
³ Department of Neurosurgery, Faculty of Health Sciences, University of Pretoria, Steve Biko Academic Hospital, Pretoria, South Africa.
⁴ Department of Neurology, Faculty of Health Sciences, University of Pretoria, Steve Biko Academic Hospital, Pretoria, South Africa.
⁵ Department of Anatomical Pathology, Faculty of Health Sciences, University of Pretoria, Steve Biko Academic Hospital, Pretoria, South Africa.

PMID: 31574329
DOI: 10.1016/j.wneu.2019.09.131

Abstract

Background: Bobble-head doll syndrome is a rare neurological syndrome presenting with repetitive anteroposterior head movements. It is usually associated with expansile cystic lesions in the third ventricular region.

Case description: An 8-year-old boy presented with involuntary bobbling head movements. Magnetic resonance imaging of the brain revealed an extensive suprasellar cyst resulting in obstructive hydrocephalus. Endoscopic ventriculo-cysto-cisternostomy resulted in improved clinical outcome.

Conclusions: Endoscopic ventriculo-cysto-cisternostomy is an effective, less-invasive technique in the treatment of suprasellar cysts that results in resolution of the bobbling head movements.

Keywords: Arachnoid cyst; Bobble-head doll syndrome; Head bobbing; Suprasellar cyst.

Publication types

Case Reports

MeSH terms

Arachnoid Cysts / diagnostic imaging
Arachnoid Cysts / etiology*
Arachnoid Cysts / surgery
Central Nervous System Cysts / complications*
Central Nervous System Cysts / diagnostic imaging
Central Nervous System Cysts / surgery
Child
Dyskinesias / diagnostic imaging
Dyskinesias / etiology*
Dyskinesias / surgery
Humans
Hydrocephalus / diagnostic imaging
Hydrocephalus / etiology*
Hydrocephalus / surgery
Magnetic Resonance Imaging
Male
Third Ventricle / abnormalities*
Third Ventricle / diagnostic imaging
Third Ventricle / surgery
Treatment Outcome
Ventriculostomy / methods*

Supplementary concepts

Bobble-head doll syndrome