Two Cases of a Prenatally Diagnosed Double Aortic Arch with Postnatal Obliteration of the Distal Left Aortic Arch

Pediatr Cardiol. 2019 Dec;40(8):1748-1751. doi: 10.1007/s00246-019-02141-z. Epub 2019 Jun 24.

Abstract

We report two cases of prenatally diagnosed double aortic arch with dominant right arch and a left-sided ductus arteriosus, consistent with a complete vascular ring. Postnatal transthoracic echocardiogram and cardiac magnetic resonance imaging demonstrated a spontaneous closure of the ductus arteriosus and obliteration of the left aortic arch distal to the origin of the left subclavian artery in both cases. Spontaneous closure of the ductus arteriosus involving extended ductal tissue in the left aortic arch likely led to obliteration of the distal left arch after birth. One patient presented with recurrent symptoms suggestive of dysphagia and underwent a successful surgical repair of the vascular ring with resolution of symptoms. The other patient has been asymptomatic and is 4 years old at the time of this report.

Keywords: Atretic left aortic arch; Cardiac magnetic resonance imaging; Double aortic arch; Fetal echocardiography; Vascular ring.

Publication types

  • Case Reports

MeSH terms

  • Child, Preschool
  • Ductus Arteriosus, Patent / complications
  • Ductus Arteriosus, Patent / diagnostic imaging*
  • Ductus Arteriosus, Patent / surgery
  • Echocardiography, Doppler, Color
  • Female
  • Gestational Age
  • Humans
  • Infant, Newborn
  • Magnetic Resonance Imaging
  • Male
  • Prenatal Diagnosis / methods*
  • Vascular Ring / complications
  • Vascular Ring / diagnostic imaging*
  • Vascular Ring / surgery