Laparoscopic nephroureterectomy as treatment in obstructed hemivagina and ipsilateral renal agenesis (OHVIRA) syndrome

Int Braz J Urol. 2019 Sep-Oct;45(5):1076-1077. doi: 10.1590/S1677-5538.IBJU.2018.0430.

Abstract

Introduction: OHVIRA syndrome is a rare entity characterized by renal and Mullerian anomalies. The objective of the video is, through a clinical case, to discuss the importance of diagnosis, management and treatment, to avoid the complications that this syndrome entails, and to improve the long-term prognosis.

Materials and methods: We report the case of a 10-year-old girl who consulted for abdominal pain, being diagnosed with OHVIRA syndrome. We describe the diagnosis and the surgical technique. In addition, we perform a systematic review in PubMed to report the published literature of this topic and we show the optimal management of this pathology.

Publication types

  • Case Reports
  • Video-Audio Media

MeSH terms

  • Abnormalities, Multiple
  • Child
  • Congenital Abnormalities / surgery*
  • Female
  • Humans
  • Kidney / abnormalities*
  • Kidney / surgery
  • Kidney Diseases / congenital*
  • Kidney Diseases / surgery
  • Laparoscopy / methods*
  • Nephroureterectomy / methods*
  • Reproducibility of Results
  • Syndrome
  • Treatment Outcome
  • Uterus / abnormalities
  • Uterus / surgery
  • Vagina / abnormalities*
  • Vagina / surgery*

Supplementary concepts

  • Hereditary renal agenesis