Wunderlich's syndrome in pregnancy: a shocking triad

BMJ Case Rep. 2019 May 19;12(5):e229219. doi: 10.1136/bcr-2019-229219.

Abstract

Wunderlich's syndrome, non-traumatic renal haemorrhage into the subscapular and perinephric space, in pregnancy, is a very rare clinical entity. We describe a case of Wunderlich's syndrome in a 29-year-old gravida 5 para 4 who presented to our emergency department with sudden onset severe left flank pain. On assessment, she was clinically shocked-hypotensive, tachycardic and perfused poorly peripherally. Ultrasound of the abdomen and pelvis and subsequent MRI of the left kidney revealed a large hypervascular exophytic lesion arising from the left renal pole-appearance consistent with an angiomyolipoma. This specific presentation is clinically characterised as Lenk's triad-acute flank pain, flank mass and hypovolaemic shock. The patient was adequately resuscitated and interventional radiological embolisation of the mass was performed. She went on to have an uneventful pregnancy and delivered vaginally after induction at 38 weeks of gestation.

Keywords: obstetrics and gynaecology; urology.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Angiomyolipoma / diagnostic imaging
  • Angiomyolipoma / pathology*
  • Angiomyolipoma / surgery
  • Delivery, Obstetric
  • Female
  • Flank Pain / etiology
  • Humans
  • Kidney Neoplasms / diagnostic imaging
  • Kidney Neoplasms / pathology*
  • Kidney Neoplasms / surgery
  • Magnetic Resonance Imaging
  • Pregnancy
  • Pregnancy Complications, Neoplastic / diagnosis
  • Pregnancy Complications, Neoplastic / pathology*
  • Pregnancy Complications, Neoplastic / surgery
  • Shock, Hemorrhagic / etiology
  • Syndrome