Dermatopathia Pigmentosa Reticularis

Indian J Dermatol. 2019 Mar-Apr;64(2):149-151. doi: 10.4103/ijd.IJD_401_17.

Abstract

Dermatopathia pigmentosa reticularis is a rare ectodermal dysplasia that presents with a triad of reticulate hyperpigmentation, nonscarring alopecia, and nail dystrophy. We report herein a case of a 23-year-old male presenting with the characteristic triad associated with anhidrosis and palmoplantar keratoderma.

Keywords: Dermatopathia pigmentosa reticularis; ectodermal dysplasia; reticulate pigmentation.

Publication types

  • Case Reports