Left sided PAPVC with intact IAS-Surgically managed with vertical vein anastomosis to LA appendage: A rare case report

Int J Surg Case Rep. 2019:59:217-219. doi: 10.1016/j.ijscr.2019.03.022. Epub 2019 Mar 28.

Abstract

Introduction: Partial anomalous pulmonary venous connection (PAPVC) is a rare entity. Only 10% of these are left sided. An intact atrial septum is further uncommon.

Presentation of case: We present a case of left sided PAPVC with no atrial septal defect (ASD), who presented with effort intolerance and an unremarkable physical examination. Computed tomography pulmonary angiography (CTPA) confirmed the primary diagnosis as suggested by an initial 2-D echocardiography, and aided in better understanding of the anatomy.

Conclusion: Patient underwent successful surgery through a simple & reproducible technique of anastomosis of vertical vein to left atrial appendage. Patient recovered uneventfully and was discharged on day 10.

Keywords: Atrial septal defect (ASD); Case report; Left atrial appendage; Partial anomalous pulmonary venous connection (PAPVC); Vertical vein.