Pulmonary Emphysema in a Child With Alpha-1 Antitrypsin Deficiency: Evaluation of 2 Years of Intravenous Augmentation Therapy
Arch Bronconeumol (Engl Ed). 2019 Sep;55(9):502-504.
doi: 10.1016/j.arbres.2019.01.009.
Epub 2019 Mar 11.
[Article in
English,
Spanish]
Affiliations
- 1 Respiratory Department, Centro Hospitalar de Trás-os-Montes e Alto Douro, Vila Real, Portugal. Electronic address: mariaestevesbrandao@gmail.com.
- 2 Respiratory Department, Centro Hospitalar de Trás-os-Montes e Alto Douro, Vila Real, Portugal.
- 3 Institute of Molecular Pathology and Immunology of the University of Porto, Porto, Portugal; Instituto de Investigação e Inovação em Saúde (I3S), Porto, Portugal.
No abstract available
MeSH terms
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Administration, Intravenous
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Humans
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Infant, Newborn
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Male
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Pulmonary Emphysema / etiology*
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Time Factors
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Treatment Outcome
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alpha 1-Antitrypsin / administration & dosage*
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alpha 1-Antitrypsin Deficiency / complications*
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alpha 1-Antitrypsin Deficiency / drug therapy*