Abstract
Immunoglobulin-G4-related disease (IgG4RD) is a novel clinical entity characterized by lymphoplasmacytic infiltrates presenting as an excessive fibrosis such as retroperitoneal inflammatory pseudotumor but rarely affecting the heart or the aorta. We describe a case of IgG4RD with multifocal aortic involvement presenting as an acute aortic syndrome.
Copyright © 2019 The Society of Thoracic Surgeons. Published by Elsevier Inc. All rights reserved.
MeSH terms
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Acute Coronary Syndrome / diagnosis*
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Acute Coronary Syndrome / surgery
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Aorta, Thoracic / diagnostic imaging*
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Aorta, Thoracic / physiopathology
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Aortic Aneurysm, Thoracic / diagnostic imaging*
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Aortic Aneurysm, Thoracic / pathology
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Aortic Aneurysm, Thoracic / surgery
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Aortography / methods
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Biopsy, Needle
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Cardiac Surgical Procedures / methods*
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Chest Pain / diagnosis
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Chest Pain / etiology
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Coronary Artery Bypass / methods
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Critical Illness
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Diagnosis, Differential
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Echocardiography, Transesophageal / methods
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Follow-Up Studies
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Granuloma, Plasma Cell / diagnostic imaging*
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Granuloma, Plasma Cell / pathology
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Granuloma, Plasma Cell / surgery
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Heart Arrest, Induced / methods
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Humans
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Immunoglobulin G / immunology
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Immunohistochemistry
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Male
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Middle Aged
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Multidetector Computed Tomography / methods*
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Sternotomy / methods
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Treatment Outcome