Immunoglobulin G4 Inflammatory Aortic Aneurysm Mimicking Acute Aortic Syndrome

Ann Thorac Surg. 2019 Sep;108(3):e179-e181. doi: 10.1016/j.athoracsur.2019.01.029. Epub 2019 Feb 13.

Abstract

Immunoglobulin-G4-related disease (IgG4RD) is a novel clinical entity characterized by lymphoplasmacytic infiltrates presenting as an excessive fibrosis such as retroperitoneal inflammatory pseudotumor but rarely affecting the heart or the aorta. We describe a case of IgG4RD with multifocal aortic involvement presenting as an acute aortic syndrome.

Publication types

  • Case Reports

MeSH terms

  • Acute Coronary Syndrome / diagnosis*
  • Acute Coronary Syndrome / surgery
  • Aorta, Thoracic / diagnostic imaging*
  • Aorta, Thoracic / physiopathology
  • Aortic Aneurysm, Thoracic / diagnostic imaging*
  • Aortic Aneurysm, Thoracic / pathology
  • Aortic Aneurysm, Thoracic / surgery
  • Aortography / methods
  • Biopsy, Needle
  • Cardiac Surgical Procedures / methods*
  • Chest Pain / diagnosis
  • Chest Pain / etiology
  • Coronary Artery Bypass / methods
  • Critical Illness
  • Diagnosis, Differential
  • Echocardiography, Transesophageal / methods
  • Follow-Up Studies
  • Granuloma, Plasma Cell / diagnostic imaging*
  • Granuloma, Plasma Cell / pathology
  • Granuloma, Plasma Cell / surgery
  • Heart Arrest, Induced / methods
  • Humans
  • Immunoglobulin G / immunology
  • Immunohistochemistry
  • Male
  • Middle Aged
  • Multidetector Computed Tomography / methods*
  • Sternotomy / methods
  • Treatment Outcome

Substances

  • Immunoglobulin G