Central nervous system-restricted familial hemophagocytic lymphohistiocytosis responds to hematopoietic cell transplantation

Blood Adv. 2019 Feb 26;3(4):503-507. doi: 10.1182/bloodadvances.2018027417.

Abstract

  1. Familial HLH can present as chronic isolated neuroinflammation.

  2. CNS-isolated HLH responds to hematopoietic cell transplantation.

Publication types

  • Case Reports
  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Brain / pathology*
  • Child
  • Female
  • Hematopoietic Stem Cell Transplantation*
  • Humans
  • Inflammation / pathology
  • Inflammation / therapy
  • Lymphohistiocytosis, Hemophagocytic / pathology
  • Lymphohistiocytosis, Hemophagocytic / therapy*
  • Transplantation, Homologous