Divergent LAG-3 versus BTLA, TIGIT, and FCRL3 expression in Sézary syndrome

Leuk Lymphoma. 2019 Aug;60(8):1899-1907. doi: 10.1080/10428194.2018.1564827. Epub 2019 Jan 14.

Abstract

In Sézary syndrome (SS) impaired T-cell function and cytokine profile lead to immune evasion. Immune checkpoints non-redundantly regulate immune responses and targeting them is promising. We evaluated the expression of BTLA, CTLA-4, FCRL3, LAG-3, and TIGIT in tumor and non-tumor SS T-cells.Compared to CD4+ T helper cells from ten healthy individuals, tumor cells of eight SS patients had a significant upregulation of BTLA (1.5-fold; p < .0001), FRCL3 (2.2-fold; p < .0028) and TIGIT (2.2-fold; p < .0003) expression. In contrast, we found a reduced expression of LAG-3+ cells in the blood of tumor patients (0.5-fold; p < .0014). Only weak alternations between tumor, non-tumor cells, and healthy controls were observed regarding CTLA-4 (0.5-fold; p < .2022). Our results show a diverse expression pattern of immune-regulatory molecules in SS patients. As these molecules are essential in the regulation of T-cell mediated tumor surveillance and defense, their specific targeting might be of clinical relevance.

Keywords: CTCL; Sézary syndrome; immune checkpoints; immune exhaustion; immunotherapy.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Aged
  • Antigens, CD / genetics*
  • Antigens, CD / metabolism
  • Biomarkers, Tumor*
  • CD4 Lymphocyte Count
  • CD4-Positive T-Lymphocytes / immunology
  • CD4-Positive T-Lymphocytes / metabolism
  • Female
  • Gene Expression Regulation, Neoplastic*
  • Humans
  • Immunophenotyping
  • Lymphocyte Activation Gene 3 Protein
  • Male
  • Middle Aged
  • Receptors, Immunologic / genetics*
  • Receptors, Immunologic / metabolism
  • Sezary Syndrome / drug therapy
  • Sezary Syndrome / genetics*
  • Sezary Syndrome / immunology

Substances

  • Antigens, CD
  • BTLA protein, human
  • Biomarkers, Tumor
  • FCRL3 protein, human
  • Receptors, Immunologic
  • TIGIT protein, human
  • Lymphocyte Activation Gene 3 Protein
  • Lag3 protein, human