Rationale: Cardiac lymphangioma is a rare disease. Until now, there have been only a few cases of cardiac lymphangioma reported in the literature.
Patient concerns: We report the case of a 57-year-old female patient with cardiac lymphangioma from atrial septum.
Diagnosis: Color Doppler echocardiography was performed, which revealed a tumor occupying a large amount of space in the left and right atrium.
Interventions: The patient underwent thoracoscopic cardiac tumor resection under general anesthesia according to the procedure used for benign tumors.
Outcomes: The patient recovered completely and was discharged home. Follow-up color Doppler echocardiography scans obtained from 6 months to 2 years after the operation showed no recurrent mass.
Lessons: Once the tumor is detected, surgical treatment should be implemented as soon as possible.