Cutaneous Sarcomas

Hematol Oncol Clin North Am. 2019 Feb;33(1):87-101. doi: 10.1016/j.hoc.2018.08.007.

Abstract

Cutaneous sarcomas are rare malignancies that may present with a variety of clinical manifestations. This article focuses on 4 of the most common cutaneous sarcomas (Kaposi sarcoma, cutaneous angiosarcoma, dermatofibrosarcoma protuberans, and cutaneous leiomyosarcoma) and reviews clinical, diagnostic, and therapeutic aspects of these rare skin malignancies.

Keywords: Angiosarcoma; Cutaneous leiomyosarcoma; Cutaneous oncology; Cutaneous sarcomas; Dermatofibrosarcoma protuberans; Kaposi sarcoma.

Publication types

  • Review

MeSH terms

  • Combined Modality Therapy
  • Diagnosis, Differential
  • Disease Management
  • Disease Susceptibility
  • Humans
  • Outcome Assessment, Health Care
  • Phenotype
  • Prognosis
  • Sarcoma / diagnosis*
  • Skin Neoplasms / diagnosis*
  • Skin Neoplasms / epidemiology
  • Skin Neoplasms / etiology
  • Skin Neoplasms / therapy