"Neuro-renal syndrome" related to anti-contactin-1 antibodies

Muscle Nerve. 2019 Mar;59(3):E19-E21. doi: 10.1002/mus.26392. Epub 2019 Jan 6.
No abstract available

Keywords: anti-contactin-1 IgG4 antibodies; anti-neurofascin-186 IgG4 antibodies; chronic inflammatory demyelinating polyradiculoneuropathy; nephrotic syndrome; nodopathy; paranodopathy.

Publication types

  • Case Reports

MeSH terms

  • Aged
  • Antibodies / immunology*
  • Contactin 1 / immunology*
  • Electrodiagnosis
  • Electromyography
  • Fatal Outcome
  • Humans
  • Immunoglobulin G / immunology
  • Kidney Diseases / diagnostic imaging
  • Kidney Diseases / etiology*
  • Kidney Diseases / immunology
  • Magnetic Resonance Imaging
  • Male
  • Muscle Weakness
  • Neural Conduction
  • Polyradiculoneuropathy, Chronic Inflammatory Demyelinating / complications
  • Polyradiculoneuropathy, Chronic Inflammatory Demyelinating / diagnostic imaging
  • Polyradiculoneuropathy, Chronic Inflammatory Demyelinating / immunology*
  • Syndrome

Substances

  • Antibodies
  • Contactin 1
  • Immunoglobulin G