Fetal Noncompaction Cardiomyopathy and Histologic Diagnosis of Spongy Myocardium: Case Report and Review of the Literature

Rev Bras Ginecol Obstet. 2018 Nov;40(11):722-725. doi: 10.1055/s-0038-1673677. Epub 2018 Oct 11.

Abstract

Noncompaction cardiomyopathy (NCCM) and left ventricular noncompaction (LVNC), in their isolated form, are rare cardiomyopathies. They are characterized by a thickened myocardium due to the presence of deep trabeculae recesses, and to thick trabeculae. This condition is associated with a variable clinical phenotype including heart failure, thromboembolism, and sudden death. We report a case of LVNC at 26 weeks and 4 days of gestation revised on the basis of what is currently reported in the literature. A review of the literature was performed to better describe this rare condition. Left ventricular noncompaction is a rare fetal condition and it should be suspected in case of cardiomyopathy.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Female
  • Heart / diagnostic imaging*
  • Humans
  • Isolated Noncompaction of the Ventricular Myocardium / diagnostic imaging*
  • Myocardium / pathology
  • Ultrasonography, Prenatal*
  • Young Adult