Emergency Ross Procedure for Pediatric Aortic Valve Myxofibrosarcoma

Mani Ram Krishna; Supreet P Marathe; Amir Maghsoudi; Geoffrey McCowage; Megan C Sherwood; Yishay Orr

doi:10.1016/j.athoracsur.2018.07.060

Emergency Ross Procedure for Pediatric Aortic Valve Myxofibrosarcoma

Ann Thorac Surg. 2019 Mar;107(3):e183-e185. doi: 10.1016/j.athoracsur.2018.07.060. Epub 2018 Sep 25.

Authors

Mani Ram Krishna¹, Supreet P Marathe¹, Amir Maghsoudi², Geoffrey McCowage³, Megan C Sherwood⁴, Yishay Orr⁵

Affiliations

¹ Heart Centre for Children, The Children's Hospital at Westmead, Westmead, New South Wales, Australia.
² Department of Pathology, The Children's Hospital at Westmead, Westmead, New South Wales, Australia.
³ Cancer Centre for Children, The Children's Hospital at Westmead, Westmead, New South Wales, Australia.
⁴ Heart Centre for Children, The Children's Hospital at Westmead, Westmead, New South Wales, Australia; School of Child and Adolescent Health, Sydney Medical School, University of Sydney, Sydney, Australia.
⁵ Heart Centre for Children, The Children's Hospital at Westmead, Westmead, New South Wales, Australia; School of Child and Adolescent Health, Sydney Medical School, University of Sydney, Sydney, Australia. Electronic address: yishay.orr@health.nsw.gov.au.

PMID: 30266618
DOI: 10.1016/j.athoracsur.2018.07.060

Abstract

Primary cardiac tumors in children are uncommon and rarely demand surgical intervention. We report a malignant tumor arising from the aortic root in a 5-year-old boy presenting with left ventricular outflow tract obstruction and tumor embolism, its surgical management using the Ross procedure, and the unique histopathological aspects of the tumor.

Publication types

Case Reports

MeSH terms

Aortic Valve
Cardiac Surgical Procedures / methods*
Child, Preschool
Echocardiography, Doppler, Color
Fibrosarcoma / diagnosis
Fibrosarcoma / surgery*
Heart Neoplasms / diagnosis
Heart Neoplasms / surgery*
Humans
Male
Positron-Emission Tomography