Management of Heart Failure in Adult Congenital Heart Disease

Abstract

There are more than 1 million adults with congenital heart disease (ACHD) in the United States. Heart failure (HF) is the most common late cardiovascular complication. These patients are challenging to manage given their diverse presentation, anatomy, and complex hemodynamics. Examination of underlying anatomy is crucial because many require late transcatheter and surgical interventions after developing HF. Management of arrhythmia is equally important because this can modify HF symptoms. A multidisciplinary team with expertise in the care of ACHD-HF is critical.

Keywords: Congenital heart disease; Fontan; Heart failure; Single ventricle dysfunction; Systemic ventricle dysfunction.