Modifying Rap1-signalling by targeting Pde6δ is neuroprotective in models of Alzheimer's disease

Mol Neurodegener. 2018 Sep 26;13(1):50. doi: 10.1186/s13024-018-0283-3.

Abstract

Background: Neuronal Ca2+ dyshomeostasis and hyperactivity play a central role in Alzheimer's disease pathology and progression. Amyloid-beta together with non-genetic risk-factors of Alzheimer's disease contributes to increased Ca2+ influx and aberrant neuronal activity, which accelerates neurodegeneration in a feed-forward fashion. As such, identifying new targets and drugs to modulate excessive Ca2+ signalling and neuronal hyperactivity, without overly suppressing them, has promising therapeutic potential.

Methods: Here we show, using biochemical, electrophysiological, imaging, and behavioural tools, that pharmacological modulation of Rap1 signalling by inhibiting its interaction with Pde6δ normalises disease associated Ca2+ aberrations and neuronal activity, conferring neuroprotection in models of Alzheimer's disease.

Results: The newly identified inhibitors of the Rap1-Pde6δ interaction counteract AD phenotypes, by reconfiguring Rap1 signalling underlying synaptic efficacy, Ca2+ influx, and neuronal repolarisation, without adverse effects in-cellulo or in-vivo. Thus, modulation of Rap1 by Pde6δ accommodates key mechanisms underlying neuronal activity, and therefore represents a promising new drug target for early or late intervention in neurodegenerative disorders.

Conclusion: Targeting the Pde6δ-Rap1 interaction has promising therapeutic potential for disorders characterised by neuronal hyperactivity, such as Alzheimer's disease.

Keywords: Alzheimer’s disease; Hyperexcitability; Neuroprotection; Pde6δ; Rap1.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Alzheimer Disease / metabolism*
  • Alzheimer Disease / pathology
  • Amyloid beta-Peptides / metabolism
  • Animals
  • Cyclic Nucleotide Phosphodiesterases, Type 6 / metabolism*
  • Disease Models, Animal
  • Humans
  • Mice, Transgenic
  • Neurons / metabolism
  • Neurons / pathology
  • Neuroprotection / physiology
  • Neuroprotective Agents / therapeutic use
  • Shelterin Complex
  • Signal Transduction / physiology
  • Telomere-Binding Proteins / metabolism*
  • rap1 GTP-Binding Proteins / metabolism*

Substances

  • Amyloid beta-Peptides
  • Neuroprotective Agents
  • Shelterin Complex
  • TERF2IP protein, human
  • Telomere-Binding Proteins
  • Cyclic Nucleotide Phosphodiesterases, Type 6
  • Rap1 protein, mouse
  • rap1 GTP-Binding Proteins