Heart specific knockout of Ndufs4 ameliorates ischemia reperfusion injury

J Mol Cell Cardiol. 2018 Oct:123:38-45. doi: 10.1016/j.yjmcc.2018.08.022. Epub 2018 Aug 27.

Abstract

Rationale: Ischemic heart disease (IHD) is a leading cause of mortality. The most effective intervention for IHD is reperfusion, which ironically causes ischemia reperfusion (I/R) injury mainly due to oxidative stress-induced cardiomyocyte death. The exact mechanism and site of reactive oxygen species (ROS) generation during I/R injury remain elusive.

Objective: We aim to test the hypothesis that Complex I-mediated forward and reverse electron flows are the major source of ROS in I/R injury of the heart.

Methods and results: We used a genetic model of mitochondrial Complex I deficiency, in which a Complex I assembling subunit, Ndufs4 was knocked out in the heart (Ndufs4H-/-). The Langendorff perfused Ndufs4H-/- hearts exhibited significantly reduced infarct size (45.3 ± 5.5% in wild type vs 20.9 ± 8.1% in Ndufs4H-/-), recovered contractile function, and maintained mitochondrial membrane potential after no flow ischemia and subsequent reperfusion. In cultured adult cardiomyocytes from Ndufs4H-/- mice, I/R mimetic treatments caused minimal cell death. Reintroducing Ndufs4 in Ndufs4H-/- cardiomyocytes abolished the protection. Mitochondrial NADH declined much slower in Ndufs4H-/- cardiomyocytes during reperfusion suggesting decreased forward electron flow. Mitochondrial flashes, a marker for mitochondrial respiration, were inhibited in Ndufs4H-/- cardiomyocytes at baseline and during I/R, which was accompanied by preserved aconitase activity suggesting lack of oxidative damage. Finally, pharmacological blockade of forward and reverse electron flow at Complex I inhibited I/R-induced cell death.

Conclusions: These results provide the first genetic evidence supporting the central role of mitochondrial Complex I in I/R injury of mouse heart. The study also suggests that both forward and reverse electron flows underlie oxidative cardiomyocyte death during reperfusion.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Biomarkers
  • Biopsy
  • Cell Death / genetics
  • Cell Respiration / genetics
  • Disease Models, Animal
  • Electron Transport Complex I / genetics*
  • Electron Transport Complex I / metabolism
  • Fluorescent Antibody Technique
  • Genetic Predisposition to Disease
  • Mice
  • Mice, Knockout
  • Mice, Transgenic
  • Mitochondria, Heart / genetics
  • Mitochondria, Heart / metabolism
  • Models, Biological
  • Myocardial Reperfusion Injury / etiology*
  • Myocardial Reperfusion Injury / metabolism*
  • Myocardial Reperfusion Injury / pathology
  • Myocardial Reperfusion Injury / physiopathology
  • Myocardium / metabolism*
  • Myocardium / pathology
  • Myocytes, Cardiac / metabolism
  • Organ Specificity / genetics
  • Oxidative Stress
  • Reactive Oxygen Species / metabolism

Substances

  • Biomarkers
  • Ndufs4 protein, mouse
  • Reactive Oxygen Species
  • Electron Transport Complex I