Urinary tract stones in cystic fibrosis

Paediatr Respir Rev. 2018 Jun:27:21-23. doi: 10.1016/j.prrv.2018.03.007. Epub 2018 Jun 18.

Abstract

Urinary tract stones are a common problem in a general population but increasingly so in cystic fibrosis (CF) patients as survival improves. Mechanisms of stone formation are discussed, particularly those unique to CF patients. Modalities of treatment and the decision making process in this choice is outlined as well as possible future preventative strategies.

Keywords: Cystic fibrosis; Hyperoxaluria; Renal stones.

Publication types

  • Review

MeSH terms

  • Cystic Fibrosis* / complications
  • Cystic Fibrosis* / metabolism
  • Cystic Fibrosis* / therapy
  • Cystic Fibrosis* / urine
  • Disease Management
  • Humans
  • Hyperoxaluria / etiology
  • Hyperoxaluria / metabolism
  • Urinary Calculi / etiology
  • Urinary Calculi / metabolism
  • Urinary Calculi / prevention & control*