Weston-Hurst syndrome with acute hemorrhagic cerebellitis

Clin Neurol Neurosurg. 2018 Oct:173:118-119. doi: 10.1016/j.clineuro.2018.08.007. Epub 2018 Aug 11.

Abstract

Weston-Hurst syndrome is an exceptional variant of ADEM characterized by brain hemorrhages. Lesions are usually supratentorial and death is a usual outcome. We report a cerebellar Weston-Hurst syndrome early treated by craniectomy, steroids and plasma exchange. This is the first case of infratentorial Weston-Hurst syndrome associated with a favorable outcome.

Keywords: Acute disseminated encephalomyelitis; Cerebellar hemorrhage; Cerebellitis; Weston-Hurst syndrome.

MeSH terms

  • Adult
  • Brain / pathology
  • Brain / surgery*
  • Cerebellar Diseases / diagnosis
  • Cerebellar Diseases / pathology
  • Cerebellar Diseases / therapy
  • Encephalomyelitis, Acute Disseminated / diagnosis
  • Encephalomyelitis, Acute Disseminated / therapy*
  • Female
  • Hemorrhage / pathology
  • Hemorrhage / therapy
  • Humans
  • Leukoencephalitis, Acute Hemorrhagic / diagnosis
  • Leukoencephalitis, Acute Hemorrhagic / therapy*
  • Magnetic Resonance Imaging / methods
  • Steroids / therapeutic use*

Substances

  • Steroids