Erdheim-Chester disease: a rare histiocytosis (case report and review of the literature)

Mahtat El Mehdi; Safae Regragui; Hicham Eddou; Selim Jennane; Hicham El Maaroufi; Kamal Doghmi; Mohamed Mikdame

doi:10.11604/pamj.2018.29.62.4088

Erdheim-Chester disease: a rare histiocytosis (case report and review of the literature)

Pan Afr Med J. 2018 Jan 22:29:62. doi: 10.11604/pamj.2018.29.62.4088. eCollection 2018.

[Article in French]

Authors

Mahtat El Mehdi¹, Safae Regragui¹, Hicham Eddou¹, Selim Jennane¹, Hicham El Maaroufi¹, Kamal Doghmi¹, Mohamed Mikdame¹

Affiliation

¹ Department of Clinical Haematology, Military Hospital of Instruction Mohamed V, Rabat, Morocco.

Abstract

We report a case of Erdheim-chester disease, a rare non-langerhans histiocytosis revealed by polydipsia-polyuria syndrome in a 26 years old woman, trated by interferon with a good response.

Publication types

Case Reports
Review

MeSH terms

Adult
Erdheim-Chester Disease / diagnosis*
Erdheim-Chester Disease / drug therapy
Female
Humans
Immunologic Factors / therapeutic use
Interferon-alpha / therapeutic use
Polydipsia / etiology*
Polyuria / etiology*
Treatment Outcome

Substances

Immunologic Factors
Interferon-alpha