Congenital malformations of the lung are extremely rare with an incidence of pulmonary hypoplasia around 1-2/12,000 births. Boyden has categorized three degrees of malformation including (i) agenesis in which there is complete absence of the lung and bronchus and no vascular supply to the affected side, (ii) aplasia in which there is the presence of rudimentary bronchus with the absence of pulmonary parenchyma, and (iii) hypoplasia in which there are variable amounts of bronchial tree, pulmonary parenchyma, and supporting vasculature. Here, we present an incidental case of pulmonary hypoplasia in a young female.
Keywords: Computed tomography; fiberoptic bronchoscopy; pulmonary angiography; pulmonary hypoplasia.