Purpose: To report the simultaneous presentation of three ocular manifestations of granulomatosis with polyangiitis in one eye.
Case report: A 42-year-old man with a confirmed diagnosis of granulomatosis with polyangiitis was referred to the emergency room with sudden blurred vision. Eye examination showed hyperemic conjunctiva due to necrotizing scleritis in the superior nasal quadrant of the left eye, a mass in the left superior lid, as well as central retinal artery occlusion in the same eye.
Conclusion: This case suggests that unilateral eye involvement may be a manifestation of underlying granulomatosis with polyangiitis.
Keywords: Central Retinal Artery Occlusion; Granulomatosis with Polyangiitis; Lid Granuloma; Necrotizing Scleritis.