Series of rare lung diseases mimicking imaging patterns of common diffuse parenchymal lung diseases

Lung India. 2018 May-Jun;35(3):231-236. doi: 10.4103/lungindia.lungindia_291_17.

Abstract

Diffuse parenchymal lung diseases (DPLDs) encompass a variety of restrictive and obstructive lung pathologies. In this article, the authors discuss a series of rare pulmonary entities and their high-resolution computed tomography imaging appearances, which can mimic more commonly encountered patterns of DPLDs. These cases highlight the importance of surgical lung biopsies in patients with imaging findings that do not show typical imaging features of usual interstitial pneumonia.

Keywords: Amyloidosis; diffuse idiopathic pulmonary neuroendocrine cell hyperplasia; pleuroparenchymal fibroelastosis; pulmonary capillary hemangiomatosis; usual interstitial pneumonia.