Atypically presenting kaposiform hemangioendothelioma of the knee: ultrasound findings

J Med Ultrason (2001). 2018 Oct;45(4):653-656. doi: 10.1007/s10396-018-0878-x. Epub 2018 Apr 10.

Abstract

Kaposiform hemangioendothelioma (KHE) is a rare vascular tumor of early childhood and infancy. Kasabach-Merritt phenomenon, a common complication of KHE, is characterized by life-threatening thrombocytopenia, hemolytic anemia, and consumption coagulopathy. There may be atypical cases that do not present with Kasabach-Merritt phenomenon and do have atypical imaging findings. Knowledge of atypical imaging features may assist radiologists in identifying KHE. In this report, we present a 4-year-old case of KHE with atypical ultrasound findings.

Keywords: Color Doppler imaging; Kaposiform hemangioendothelioma; Soft-tissue mass; Ultrasonography; Vascular tumor.

Publication types

  • Case Reports

MeSH terms

  • Child, Preschool
  • Diagnosis, Differential
  • Female
  • Hemangioendothelioma / diagnostic imaging*
  • Hemangioendothelioma / pathology
  • Hemangioendothelioma / surgery
  • Humans
  • Kasabach-Merritt Syndrome / diagnostic imaging*
  • Kasabach-Merritt Syndrome / pathology
  • Kasabach-Merritt Syndrome / surgery
  • Knee
  • Sarcoma, Kaposi / diagnostic imaging*
  • Sarcoma, Kaposi / pathology
  • Sarcoma, Kaposi / surgery
  • Vascular Neoplasms / diagnostic imaging*
  • Vascular Neoplasms / pathology
  • Vascular Neoplasms / surgery

Supplementary concepts

  • Kaposiform Hemangioendothelioma