Retinal vasproliferative tumor in a case of X-linked retinoschisis detachment

Nimesh A Patel; Diana Laura; Kimberly D Tran; Stanley Chang; Gaetano Barile; Audina M Berrocal

doi:10.1016/j.ajoc.2018.01.002

Retinal vasproliferative tumor in a case of X-linked retinoschisis detachment

Am J Ophthalmol Case Rep. 2018 Jan 4:9:48-50. doi: 10.1016/j.ajoc.2018.01.002. eCollection 2018 Mar.

Authors

Nimesh A Patel¹, Diana Laura¹, Kimberly D Tran¹, Stanley Chang², Gaetano Barile³, Audina M Berrocal¹

Affiliations

¹ Department of Ophthalmology, Bascom Palmer Eye Institute, 900 NW17th St., Miami, FL 33136, USA.
² Department of Ophthalmology, Edward S. Harkness Eye Institute, 635 W 165th St., New York, NY 10032, USA.
³ Department of Ophthalmology, Manhattan Eye, Ear, & Throat Hospital, 210 E 64th St. #3, New York, NY 10065, USA.

Abstract

Purpose: To describe the first published case of X-linked retinoschisis (XLRS) detachment with retinal vasoproliferative tumor (RVPT) and provide a literature review of the subject.

Observations: The authors describe a case of a 17 year old male with X-linked retinoschisis who presented with a retinal detachment and a retinal vasoproliferative tumor. The patient was treated with pars plana vitrectomy, endolaser, subtenon's kenalog and anti-VEGF (vascular endothelial growth factor) intravitreal injections. He regained 20/60 vision with a flat macula and had significant resolution of the associated vasoproliferative leakage seen on fluorescein angiography.

Conclusions and importance: This case adds XLRS to the conditions associated with RVPT and gives support for treatment with laser photocoagulation and anti-VEGF therapy with bevacizumab to control the exudative process.

Keywords: Retinal detachment; Vasproliferative tumor; X-linked retinoschisis.

Publication types

Case Reports