Abstract
Introduction:
Myelin oligodendrocyte glycoprotein antibodies (MOG-IgG) associated disorders present with a spectrum of clinical pictures including brainstem involvement.
Case report:
A patient with the sudden onset of a post-partum severe rhombencephalitis causing respiratory failure (12 years after a mild transverse myelitis). Despite the aggressive clinical course, she had an impressive recovery after plasmapheresis, and no further relapses on immunosuppression.
Conclusion:
MOG-IgG disorders could relapse several years after onset and involve brainstem. Good prognosis is possible after treatment.
Keywords:
Autoimmune rhombencephalitis; Brainstem in NMOSD; MOG-IgG.
Copyright © 2018 Elsevier B.V. All rights reserved.
MeSH terms
-
Adult
-
Autoantibodies / blood*
-
Demyelinating Autoimmune Diseases, CNS / complications
-
Demyelinating Autoimmune Diseases, CNS / diagnostic imaging
-
Demyelinating Autoimmune Diseases, CNS / immunology*
-
Demyelinating Autoimmune Diseases, CNS / therapy
-
Encephalitis / complications
-
Encephalitis / diagnostic imaging
-
Encephalitis / immunology*
-
Encephalitis / therapy
-
Female
-
Humans
-
Immunoglobulin G / blood*
-
Myelin-Oligodendrocyte Glycoprotein / immunology*
-
Myelitis, Transverse / complications
-
Myelitis, Transverse / diagnostic imaging
-
Myelitis, Transverse / immunology*
-
Myelitis, Transverse / therapy
-
Postpartum Period
-
Respiratory Insufficiency / etiology
-
Respiratory Insufficiency / immunology
-
Respiratory Insufficiency / therapy
-
Rhombencephalon / diagnostic imaging
-
Rhombencephalon / immunology
Substances
-
Autoantibodies
-
Immunoglobulin G
-
MOG protein, human
-
Myelin-Oligodendrocyte Glycoprotein