MOG-antibody demyelinating diseases: a case of post-partum severe rhombencephalitis and transverse myelitis

Mult Scler Relat Disord. 2018 Apr:21:9-10. doi: 10.1016/j.msard.2018.02.006. Epub 2018 Feb 8.

Abstract

Introduction: Myelin oligodendrocyte glycoprotein antibodies (MOG-IgG) associated disorders present with a spectrum of clinical pictures including brainstem involvement.

Case report: A patient with the sudden onset of a post-partum severe rhombencephalitis causing respiratory failure (12 years after a mild transverse myelitis). Despite the aggressive clinical course, she had an impressive recovery after plasmapheresis, and no further relapses on immunosuppression.

Conclusion: MOG-IgG disorders could relapse several years after onset and involve brainstem. Good prognosis is possible after treatment.

Keywords: Autoimmune rhombencephalitis; Brainstem in NMOSD; MOG-IgG.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Autoantibodies / blood*
  • Demyelinating Autoimmune Diseases, CNS / complications
  • Demyelinating Autoimmune Diseases, CNS / diagnostic imaging
  • Demyelinating Autoimmune Diseases, CNS / immunology*
  • Demyelinating Autoimmune Diseases, CNS / therapy
  • Encephalitis / complications
  • Encephalitis / diagnostic imaging
  • Encephalitis / immunology*
  • Encephalitis / therapy
  • Female
  • Humans
  • Immunoglobulin G / blood*
  • Myelin-Oligodendrocyte Glycoprotein / immunology*
  • Myelitis, Transverse / complications
  • Myelitis, Transverse / diagnostic imaging
  • Myelitis, Transverse / immunology*
  • Myelitis, Transverse / therapy
  • Postpartum Period
  • Respiratory Insufficiency / etiology
  • Respiratory Insufficiency / immunology
  • Respiratory Insufficiency / therapy
  • Rhombencephalon / diagnostic imaging
  • Rhombencephalon / immunology

Substances

  • Autoantibodies
  • Immunoglobulin G
  • MOG protein, human
  • Myelin-Oligodendrocyte Glycoprotein