We report a case of a rare mesenchymal foreskin tumor. A slow-growing node was detected during the urological examination of a 39-year-old man. A histological examination following the node excision showed a superficial leiomyosarcoma. Superficial leiomyosarcomas rarely metastasize and are associated with a better prognosis than deeper tumors. The patient had no relapse 9 months after a successful radical circumcision. We strongly recommend a histological examination whenever a growing node in the genital area is found.
Keywords: Circumcision; Mesenchymal tumor; Neoplasm; Penis tumor; Soft tissue tumor.