Pigmented Epithelioid Melanocytoma of the Cheek, Orbit, and Intracranial Cavity: A Case Report

Erik R Johnson; Michael E Korchak; Todd A Goodglick; Jasbir S Johal; Craig R Dufresne; Sina J Sabet

doi:10.1159/000477734

Pigmented Epithelioid Melanocytoma of the Cheek, Orbit, and Intracranial Cavity: A Case Report

Ocul Oncol Pathol. 2017 Dec;4(1):57-60. doi: 10.1159/000477734. Epub 2017 Jul 26.

Authors

Erik R Johnson¹, Michael E Korchak², Todd A Goodglick¹, Jasbir S Johal³, Craig R Dufresne⁴, Sina J Sabet¹

Affiliations

¹ Department of Ophthalmology, MedStar Georgetown University Hospital, Washington, DC.
² Department of Ophthalmology, MedStar Washington Hospital Center, Washington, DC.
³ INOVA Pathology Institute, Falls Church, VA, USA.
⁴ Department of Plastic Surgery, INOVA Fairfax Hospital, Falls Church, VA, USA.

Abstract

Pigmented epithelioid melanocytoma (PEM) of the skin has been rarely reported in ophthalmology. The purpose of this case report is to present a young male born with a progressive, hyperpigmented lesion involving the orbit and intracranial cavity diagnosed as PEM. The case is unique given the young age and the size, multifocality, and growth of this tumor. Identification of this lesion is paramount due to its low-grade malignant potential.

Keywords: Orbit; Pathology; Pediatrics; Pigmented epithelioid melanocytoma; Surgery.