Rare Tumors and Lesions of the Pancreas

Surg Clin North Am. 2018 Feb;98(1):169-188. doi: 10.1016/j.suc.2017.09.013.

Abstract

There are a few entities that account for most solid and cystic masses of the pancreas. The pancreas harbors a wide array of diseases, including adenocarcinoma, and its variants, such as anaplastic and adenosquamous carcinoma. Other neoplasms include acinar cell carcinoma, solid pseudopapillary tumor, and sarcomas. Benign lesions include hamartomas, hemangiomas, lymphangioma, and plasmacytoma. Isolated metastases include renal cell carcinoma, melanoma, and other carcinomas. Benign inflammatory conditions, such as autoimmune pancreatitis and groove pancreatitis can also mimic solid neoplasms of the pancreas.

Keywords: Acinar cell carcinoma; Adenosquamous carcinoma; Anaplastic carcinoma; Pancreatectomy; Pancreatic neoplasm; Primary pancreatic lymphoma; Solid pseudopapillary tumor; Unusual pancreas tumors.

Publication types

  • Review

MeSH terms

  • Diagnosis, Differential
  • Diagnostic Imaging / methods*
  • Humans
  • Pancreatic Neoplasms / diagnosis*
  • Rare Diseases*