Pancreatitis and pancreatic cystosis in Cystic Fibrosis

J Cyst Fibros. 2017 Nov:16 Suppl 2:S79-S86. doi: 10.1016/j.jcf.2017.07.004.

Abstract

The pathologic effects of an altered cystic fibrosis transmembrane receptor (CFTR) protein on the exocrine pancreas is ubiquitous and of varying severity. In this section, pancreatitis and pancreatic cystosis are covered.

Keywords: CFTR; Pancreatic cystosis, cystic fibrosis; Pancreatitis.

Publication types

  • Review

MeSH terms

  • Cystic Fibrosis / complications*
  • Cystic Fibrosis Transmembrane Conductance Regulator / metabolism*
  • Humans
  • Pancreas, Exocrine / metabolism
  • Pancreatitis* / diagnosis
  • Pancreatitis* / etiology
  • Pancreatitis* / physiopathology
  • Pancreatitis* / therapy

Substances

  • Cystic Fibrosis Transmembrane Conductance Regulator