Syringo-Subarachnoid Shunt for the Treatment of Persistent Syringomyelia Following Decompression for Chiari Type I Malformation: Surgical Results

World Neurosurg. 2017 Dec:108:836-843. doi: 10.1016/j.wneu.2017.08.002. Epub 2017 Aug 12.

Abstract

Background: Approximately 30% of patients treated with foramen magnum decompression (FMD) for Chiari I-associated syringomyelia will show persistence, recurrence, or progression of the syrinx.

Objective: This study evaluates the clinical and radiologic outcomes of syringo-subarachnoid shunt (SSS) as the treatment for persistent syringomyelia after FMD.

Methods: Data were collected retrospectively. The primary outcome measurement was neurologic function (assessed with the Modified Japanese Orthopedic Association [mJOA] scale). Secondary outcome measurements were surgical complications, reoperation rate, and syrinx status on magnetic resonance imaging (MRI).

Results: Twenty-one patients (14 females [66.7%]) underwent SSS, either concurrent to the FMD or at a later stage. Two minor surgical complications were seen: a wound dehiscence and postoperative kyphosis, both requiring revision surgery. No major complication or mortality occurred. The median change in the mJOA score was an improvement of 3 out of a possible 17 points on the scale (mean follow-up, 24.9 months). Expressed as a percentage, overall improvement was 11.8% (95% confidence interval [CI], 5.9-17.6; P < 0.001). On postoperative MRI, shrinkage of the syrinx was seen in all but 1 patient in whom the syrinx remained unchanged. Expressed as percentage, the improvement of the syrinx surface was 76.3% (95% CI, 65.0-87.7; P < 0.001), and the improvement of syrinx span was 36.4% (95% CI, 21.8-50.9; P = 0.05).

Conclusion: SSS for persistent, recurrent, or increasing syrinx following FMD for Chiari I malformation is a safe and effective surgical treatment when performed selectively by an experienced neurosurgeon.

Keywords: Chiari I malformation; Electrophysiologic monitoring; Foramen magnum decompression; Posterior columns; Spinal cord; Syringo-subarachnoid shunt; Syringomyelia.

MeSH terms

  • Adolescent
  • Adult
  • Arnold-Chiari Malformation / diagnostic imaging
  • Arnold-Chiari Malformation / surgery*
  • Cerebrospinal Fluid Shunts / methods*
  • Child
  • Child, Preschool
  • Decompression, Surgical / methods*
  • Disease Progression
  • Female
  • Humans
  • Kyphosis / epidemiology
  • Magnetic Resonance Imaging
  • Male
  • Middle Aged
  • Postoperative Complications
  • Retrospective Studies
  • Subarachnoid Space / surgery*
  • Surgical Wound Dehiscence / epidemiology
  • Syringomyelia / diagnostic imaging
  • Syringomyelia / surgery*
  • Young Adult

Supplementary concepts

  • Chiari Malformation Type I with Syringomyelia