Treatment of calmodulinopathy with verapamil

BMJ Case Rep. 2017 Aug 7:2017:bcr2017220568. doi: 10.1136/bcr-2017-220568.

Abstract

Pathological variants in genes encoding calmodulin are associated with severe clinical presentations, including recurrent ventricular fibrillation and sudden death. Beta-receptor antagonists (beta-blockers) and sodium-channel antagonists have been reported as pharmacotherapies in these disorders; however, recent data have demonstrated the importance of derangements in calcium channel inactivation. We report a sustained attempt to use calcium-channel antagonists to treat calmodulinopathy and review the treatment strategies reported in the literature to date.

Keywords: arrhythmias; cardiovascular medicine.

Publication types

  • Case Reports

MeSH terms

  • Calcium Channel Blockers / therapeutic use*
  • Calmodulin*
  • Child, Preschool
  • Humans
  • Long QT Syndrome / drug therapy*
  • Long QT Syndrome / genetics
  • Male
  • Ventricular Fibrillation / drug therapy*
  • Ventricular Fibrillation / genetics
  • Verapamil / therapeutic use*

Substances

  • Calcium Channel Blockers
  • Calmodulin
  • Verapamil