Masson's tumor of the pineal region: case report

J Neurosurg. 2018 Jun;128(6):1725-1730. doi: 10.3171/2017.2.JNS162350. Epub 2017 Aug 4.

Abstract

Intracranial intravascular papillary endothelial hyperplasia (IPEH), also referred to as Masson's tumor, is a condition that rarely occurs in the nervous system. IPEH most frequently occurs extracranially in the skin of the face, skull, neck, and trunk and can easily be mistaken clinically, radiologically, and histologically for angiosarcoma, organizing hematoma, or other vascular malformations. IPEH accounts for roughly 2% of all vascular tumors and is extremely rare intracranially, with only 23 reported cases compared with more than 300 cases of IPEH occurring in the skin and subcutaneous tissue. To date, it has never been reported to occur in the pineal region. The authors report the case of a patient with an IPEH in the pineal region who underwent complex resection and experienced reversal of neurological symptoms.

Keywords: IPEH; IPEH = intravascular papillary endothelial hyperplasia; Masson’s tumor; hemangioma; intracranial tumor; intravascular papillary endothelial hyperplasia; malignant angiosarcoma; oncology; vascular lesions.

Publication types

  • Case Reports

MeSH terms

  • Central Nervous System Vascular Malformations / pathology
  • Central Nervous System Vascular Malformations / rehabilitation
  • Central Nervous System Vascular Malformations / surgery*
  • Disease Progression
  • Endothelium, Vascular / pathology
  • Humans
  • Hyperplasia / pathology
  • Hyperplasia / rehabilitation
  • Hyperplasia / surgery*
  • Magnetic Resonance Imaging
  • Male
  • Neurosurgical Procedures
  • Pineal Gland / pathology
  • Pineal Gland / surgery*
  • Reoperation
  • Treatment Outcome
  • Young Adult