Primary pulmonary myxoid sarcoma located in interlobar fissure without parenchymal invasion

Thorac Cancer. 2017 Sep;8(5):535-538. doi: 10.1111/1759-7714.12469. Epub 2017 Jul 19.

Abstract

Primary pulmonary myxoid sarcoma (PPMS), classified as low to intermediate grade malignant myxoid endobronchial tumor, is rarely reported. Most reported cases occurred in lung parenchyme with an endobronchial component. Herein, we report a case of PPMS in a 29-year-old woman that developed in a major fissure of the left lung without parenchymal invasion. Histopathologically, the diagnosis was compatible to PPMS with EWSR1-CREB1 translocation.

Keywords: Myxoid sarcoma; pulmonary; thoracoscopy/VATS.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Female
  • Humans
  • Lung Neoplasms / diagnostic imaging*
  • Lung Neoplasms / genetics
  • Lung Neoplasms / surgery
  • Oncogene Proteins, Fusion / genetics
  • Sarcoma / diagnostic imaging*
  • Sarcoma / genetics
  • Sarcoma / surgery
  • Thoracic Surgical Procedures
  • Tomography, X-Ray Computed

Substances

  • EWSR1-CREB1 fusion protein, human
  • Oncogene Proteins, Fusion